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Research Article
October 2016

Joint Engagement and Early Language in Young Children With Fragile X Syndrome

Publication: Journal of Speech, Language, and Hearing Research
Volume 59, Number 5
Pages 1087-1098

Abstract

Purpose

In this study, we examine joint engagement (JE) in young children with fragile X syndrome (FXS) and its relationship to language abilities and autism spectrum disorder symptomatology at 24 to 36 months (toddler period) and 59 to 68 months (child period).

Method

Participants were 28 children with FXS (24 boys, four girls) and their mothers. Videotaped home observations were conducted during the toddler period and coded for JE. Language abilities were measured at both ages from a developmental assessment, a functional measure, and from a language sample. The Childhood Autism Rating Scale (Schopler, Reichler, & Renner, 1988) was completed at both ages.

Results

Children with FXS spent more time in supported JE than in coordinated JE. Using a weighted JE variable, we found that children with FXS who had higher weighted JE scores also had more advanced expressive language skills at both the toddler and child periods. Weighted JE was negatively related to autism symptomatology in the toddler period.

Conclusion

This study provides evidence that children with FXS who use more JE also have more advanced expressive language skills in early development. Therefore, existing early interventions that target JE behaviors may be effective for promoting language, social communication, and social interaction in this population.

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Published In

Journal of Speech, Language, and Hearing Research
Volume 59Number 5October 2016
Pages: 1087-1098
PubMed: 27681878

History

  • Received: Jan 5, 2015
  • Revised: May 26, 2015
  • Accepted: Feb 9, 2016
  • Published in issue: Oct 1, 2016

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Authors

Affiliations

Laura J. Hahn
Life Span Institute, University of Kansas, Lawrence
Nancy C. Brady
Kandace K. Fleming
Life Span Institute, University of Kansas, Lawrence
Steven F. Warren

Notes

Disclosure: The authors have declared that no competing interests existed at the time of publication.
Correspondence to Laura J. Hahn, who is now at the University of Illinois at Urbana-Champaign: [email protected]
Editor: Rhea Paul
Associate Editor: Linda Watson

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